Angiomyolipoma of the Perinephric Space: Case Report

Wunderlich syndrome following rupture of a renal angiomyolipoma.

Ann Saudi Med 2006;26(4):310-312 Wunderlich syndrome refers to spontaneous non-traumatic renal bleeding into the subcapsular and/or perirenal space. The appropriate treatment for this condition depends on the diagnosis of perinephric hemorrhage and the determination of its cause. Radiology therefore plays an important role in the evaluation of patients with this clinical problem. We present the...

A novel case of quartet tumor: meningioma, angiomyolipoma, ependymoma and sarcoma: report of a case and review of the literature

Multiple primary tumors in a single patient are relatively rare when four or more distinct lesions are considered. Herein, we report a case of woman with four different primary tumors: meningioma, renal angiomyolipoma, spinal ependymoma and high-grade soft tissue sarcoma. There was no family history and hereditary syndrome. The genetic analysis was completely normal. To best of our knowledge, t...

Radiological diagnosis of perinephric pathology: pictorial essay 2015

The perinephric space, shaped as an inverted cone, sits between the anterior and posterior renal fasciae. It can play host to a variety of clinical conditions encountered daily in the reporting schedule for a radiologist. Lesions may be classified and diagnosed based on their imaging characteristics, location and distribution. A broad range of differential diagnoses can be attributed to patholo...

Giant Angiomyolipoma of the Kidney with Perinephric Extension: A Rare Case

Spontaneous Perinephric Haemorrhage (Wunderlich Syndrome) Secondary to Upper Pole Renal Angiomyolipoma: A Rare Life Threatening Situation

Wunderlich Syndrome is a rare condition in which spontaneous renal haemorrhage occurs into the subcapsular and perirenal spaces in absence of trauma. It can present as a life threatening situation with profound shock which demands urgent attention. Though angiomyolipoma of the kidney is the most common neoplasm associated with spontaneous renal haemorrhage, varied presentation and lack of suspi...